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ICD-10 CM Code E71.3
E71
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71.3
Disorders of fatty-acid metabolism
E71.30
Disorder of fatty-acid metabolism, unspecified
E71.31
Disorders of fatty-acid oxidation
E71.32
Disorders of ketone metabolism
E71.39
Other disorders of fatty-acid metabolism
Excludes Type 1
peroxisomal disorders (E71.5)
Refsum's disease (G60.1)
Schilder's disease (G37.0)
Excludes Type 2
carnitine deficiency due to inborn error of metabolism (E71.42)
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